Sprengel’s deformity

Authors:

Sanz Álvarez D^a, Manuel Enguídanos MJ^b

^aMir-Pediatría. Hospital Universitario 12 de Octubre. Madrid. España.
^bPediatra. CS Los Rosales. Madrid. España.

Correspondence: D Sanz. Email: debora_sanz@hotmail.com

Reference of this article.:

Sanz Álvarez D, Manuel Enguídanos MJ. Deformidad de Sprengel. Rev Pediatr Aten Primaria. 2009;11:631-8.

Published in Internet: 31/12/2009

Abstract:

Sprengel’s deformity is characterized by congenital elevation of the scapula. It is the most common congenital malformation of the shoulder girdle. Congenital elevation of the scapula is caused by an interruption in the normal embryonic caudal migration of the scapula, so that it rests in a high position in relation to the thorax and neck.

We report the case of 4 month infant, in whom Sprengel’s deformity in the left side was detected in the 1 month well child review. It was associated with other malformations such as congenital scoliosis, renal, thoracic and vertebral abnormalities.

Keywords: Scapula abnormalities. Idiophatic scoliosis.